{"id":3665,"date":"2026-07-10T16:36:42","date_gmt":"2026-07-10T14:36:42","guid":{"rendered":"https:\/\/www.amyloidosisalliance.org\/andere-soorten\/"},"modified":"2026-11-03T08:41:40","modified_gmt":"2026-11-03T07:41:40","slug":"andere-soorten","status":"publish","type":"page","link":"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/andere-soorten\/","title":{"rendered":"Andere soorten"},"content":{"rendered":"\n<nav class=\"wp-block-group aa-breadcrumb is-layout-flow wp-block-group-is-layout-flow\" aria-label=\"Breadcrumb\">\n\t\n\t<div class=\"aa-inner\"><a href=\"\/\">Home<\/a><span class=\"aa-breadcrumb__sep\">\u203a<\/span><span class=\"aa-breadcrumb__label\">Amylo\u00efdose<\/span><span class=\"aa-breadcrumb__sep\">\u203a<\/span><a href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/\">Soorten amylo\u00efdose<\/a><span class=\"aa-breadcrumb__sep\">\u203a<\/span><span class=\"aa-breadcrumb__current\">Andere soorten<\/span><\/div>\n\t\n<\/nav>\n\n<section class=\"wp-block-group aa-page-hero is-layout-flow wp-block-group-is-layout-flow\">\n\t\n\t<div class=\"wp-block-group aa-inner is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\n\t\t<div class=\"wp-block-group aa-page-hero__grid is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\n\t\t\t<div class=\"wp-block-group is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<p class=\"aa-overline wp-block-paragraph\">Soorten amylo\u00efdose<\/p>\n\t\t\t\t<h1 class=\"wp-block-heading\">Andere soorten<\/h1>\n\t\t\t\t<p class=\"aa-lead wp-block-paragraph\">AL-, AA- en ATTR-amylo\u00efdose zijn de meest erkende systemische vormen van amylo\u00efdose. Andere vormen zijn onder meer zeldzame erfelijke amylo\u00efdosen en gelokaliseerde amylo\u00efdose. Twee situaties vallen buiten die beschrijving: erfelijke eiwitten anders dan transthyretine, en afzettingen die het orgaan waarin ze zijn ontstaan nooit verlaten. Ze hebben weinig gemeen, behalve dat het allebei uitzonderingen zijn en dat ze allebei afhangen van een nauwkeurige diagnose.<\/p>\n\t\t\t<\/div>\n\t\t\t\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-page-hero__photo is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<figure class=\"wp-block-image size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"683\" src=\"https:\/\/www.amyloidosisalliance.org\/wp-content\/uploads\/2026\/09\/the-objective-lens-of-a-microscope-above-a-slide-1024x683.jpg\" alt=\"Het objectief van een microscoop boven een objectglaasje\" class=\"wp-image-679\" srcset=\"https:\/\/www.amyloidosisalliance.org\/wp-content\/uploads\/2026\/09\/the-objective-lens-of-a-microscope-above-a-slide-1024x683.jpg 1024w, https:\/\/www.amyloidosisalliance.org\/wp-content\/uploads\/2026\/09\/the-objective-lens-of-a-microscope-above-a-slide-300x200.jpg 300w, https:\/\/www.amyloidosisalliance.org\/wp-content\/uploads\/2026\/09\/the-objective-lens-of-a-microscope-above-a-slide-768x512.jpg 768w, https:\/\/www.amyloidosisalliance.org\/wp-content\/uploads\/2026\/09\/the-objective-lens-of-a-microscope-above-a-slide-1536x1024.jpg 1536w\" sizes=\"auto, (max-width: 1024px) 100vw, 1024px\" \/><\/figure>\n\t\t\t<\/div>\n\t\t\t\n\t\t<\/div>\n\t\t\n\t<\/div>\n\t\n<\/section>\n\n<section class=\"wp-block-group aa-section aa-section--white aa-what is-layout-flow wp-block-group-is-layout-flow\" id=\"what\">\n\t\n\t<div class=\"wp-block-group aa-inner is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\n\t\t<div class=\"wp-block-group is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<p class=\"aa-section-num wp-block-paragraph\">01<\/p>\n\t\t\t<h2 class=\"wp-block-heading\">De uitzonderingen<\/h2>\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-key-idea is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<p class=\"aa-key-idea__label wp-block-paragraph\">Om te onthouden<\/p>\n\t\t\t\t<p class=\"wp-block-paragraph\">Beide zijn zeldzaam, en geen van beide is alleen aan de symptomen te herkennen. In beide gevallen maakt pas het nauwkeurig vaststellen van wat er is afgezet, en waar, behandeling mogelijk.<\/p>\n\t\t\t<\/div>\n\t\t\t\n\t\t<\/div>\n\t\t\n\t\t\n\t\t<div class=\"wp-block-group aa-what-cols is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-what-col is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<h4 class=\"wp-block-heading\">Naast de veelvoorkomende vormen<\/h4>\n\t\t\t\t<p class=\"wp-block-paragraph\">AL-amylo\u00efdose, AA-amylo\u00efdose en amylo\u00efdose door TTR zijn verantwoordelijk voor de overgrote meerderheid van de amylo\u00efdosen, en elk heeft een eigen pagina. Wat overblijft, zijn vormen die zo zeldzaam zijn dat de meeste artsen er nooit een zullen zien.<\/p>\n\t\t\t\t<p class=\"wp-block-paragraph\">Juist die zeldzaamheid is de moeilijkheid. Geen van de twee hier beschreven vormen kondigt zich aan; beide worden meestal ontdekt terwijl men naar iets heel anders zocht.<\/p>\n\t\t\t<\/div>\n\t\t\t\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-what-col is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<h4 class=\"wp-block-heading\">Waarom ze hier samen staan<\/h4>\n\t\t\t\t<p class=\"wp-block-paragraph\">Niet omdat ze op elkaar lijken: dat doen ze niet. De ene is erfelijk en tast de nieren aan; de andere is verworven en blijft in \u00e9\u00e9n orgaan.<\/p>\n\t\t\t\t<p class=\"wp-block-paragraph\">Ze staan samen omdat elk buiten de gangbare beschrijving van een amylo\u00efdose valt, en omdat in beide gevallen het laboratorium, en niet het lichamelijk onderzoek, het laatste woord heeft.<\/p>\n\t\t\t<\/div>\n\t\t\t\n\t\t<\/div>\n\t\t\n\t<\/div>\n\t\n<\/section>\n\n<section class=\"wp-block-group aa-section aa-section--cream aa-tp-duo-sec is-layout-flow wp-block-group-is-layout-flow\" id=\"forms\">\n\t\n\t<div class=\"wp-block-group aa-inner is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\n\t\t<div class=\"wp-block-group aa-centered-head is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<p class=\"aa-section-num wp-block-paragraph\">02<\/p>\n\t\t\t<h2 class=\"wp-block-heading\">Twee uitzonderingen<\/h2>\n\t\t\t<div class=\"aa-divider-dot\"><\/div>\n\t\t\t<p class=\"wp-block-paragraph\">Bij de ene gaat het om welk eiwit. Bij de andere om hoe ver het zich verspreidt.<\/p>\n\t\t<\/div>\n\t\t\n\t\t\n\t\t<div class=\"wp-block-group aa-tp-duo is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-tp-duo__card is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<p class=\"aa-tp-duo__tag wp-block-paragraph\">ZELDZAAM ERFELIJK<\/p>\n\t\t\t\t<h3 class=\"wp-block-heading\">Erfelijke eiwitten anders dan TTR<\/h3>\n\t\t\t\t<p class=\"wp-block-paragraph\">Mutaties in de alfaketen van fibrinogeen, de apolipoprote\u00efnen, lysozym of gelsoline. Ze erven allemaal autosomaal dominant over, en de nieren zijn het belangrijkste doelwit.<\/p>\n\t\t\t\t<p class=\"wp-block-paragraph\">De symptomen kunnen van de ene vorm tot de andere identiek zijn, terwijl de behandelingen niets gemeen hebben.<\/p>\n\t\t\t\t\n<div class=\"wp-block-buttons is-layout-flex wp-block-buttons-is-layout-flex\"><div class=\"wp-block-button aa-btn aa-btn--teal\"><a class=\"wp-block-button__link wp-element-button\" href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/zeldzame-erfelijke-amyloidosen\/\">Zeldzame erfelijke vormen \u2192<\/a><\/div><\/div>\n\n\t\t\t<\/div>\n\t\t\t\n\t\t\t\n\t\t\t<div class=\"wp-block-group aa-tp-duo__card is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t\t<p class=\"aa-tp-duo__tag wp-block-paragraph\">GELOKALISEERD<\/p>\n\t\t\t\t<h3 class=\"wp-block-heading\">Afzettingen beperkt tot \u00e9\u00e9n orgaan<\/h3>\n\t\t\t\t<p class=\"wp-block-paragraph\">Meestal AL-amylo\u00efd, met dezelfde lichte ketens als bij de systemische ziekte, maar aangemaakt door plasmacellen in het orgaan zelf. Er komt niets in de bloedbaan terecht, dus er wordt nergens anders iets afgezet.<\/p>\n\t\t\t\t<p class=\"wp-block-paragraph\">De luchtwegen en de blaas zijn de meest voorkomende plaatsen, en de behandeling is plaatselijk.<\/p>\n\t\t\t\t\n<div class=\"wp-block-buttons is-layout-flex wp-block-buttons-is-layout-flex\"><div class=\"wp-block-button aa-btn aa-btn--teal\"><a class=\"wp-block-button__link wp-element-button\" href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/gelokaliseerde-amyloidose\/\">Gelokaliseerde amylo\u00efdose \u2192<\/a><\/div><\/div>\n\n\t\t\t<\/div>\n\t\t\t\n\t\t<\/div>\n\t\t\n\t\t\n\t\t<div class=\"wp-block-group aa-tp-note is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<p class=\"wp-block-paragraph\">In beide gevallen wordt de biopsie vaak genomen om iets anders uit te sluiten, en wordt het amylo\u00efd bij toeval gevonden. Wat volgt (het typeren van het eiwit, het vaststellen hoe ver het zich heeft verspreid) bepaalt de behandeling.<\/p>\n\t\t<\/div>\n\t\t\n\t\t\n\t\t<div class=\"wp-block-group aa-tp-disclaimer is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<p class=\"wp-block-paragraph\">Deze pagina bevat algemene informatie voor pati\u00ebnten, families en zorgverleners. Ze vervangt geen medisch advies. Bespreek uw situatie altijd met uw eigen gespecialiseerde behandelteam.<\/p>\n\t\t<\/div>\n\t\t\n\t<\/div>\n\t\n<\/section>\n\n<section class=\"wp-block-group aa-next aa-next--split is-layout-flow wp-block-group-is-layout-flow\">\n\t\n\t<div class=\"wp-block-group aa-inner is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\n\t\t<div class=\"wp-block-group aa-next__head is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<p class=\"aa-section-num wp-block-paragraph\">Verder lezen<\/p>\n\t\t\t<h2 class=\"wp-block-heading\">De veelvoorkomende vormen<\/h2>\n\t\t<\/div>\n\t\t\n\t\t\n\t\t<div class=\"wp-block-group aa-next__grid is-layout-flow wp-block-group-is-layout-flow\">\n\t\t\t<div class=\"wp-block-group aa-next-card is-layout-flow wp-block-group-is-layout-flow\"><h3 class=\"wp-block-heading\"><a href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/al-amyloidose\/\">AL-amylo\u00efdose<\/a><\/h3><p class=\"wp-block-paragraph\">De meest voorkomende systemische vorm, veroorzaakt door lichte ketens die in het beenmerg worden aangemaakt.<\/p><\/div>\n\t\t\t<div class=\"wp-block-group aa-next-card is-layout-flow wp-block-group-is-layout-flow\"><h3 class=\"wp-block-heading\"><a href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/aa-amyloidose\/\">AA-amylo\u00efdose<\/a><\/h3><p class=\"wp-block-paragraph\">Een complicatie van langdurige ontsteking, die vooral de nieren treft.<\/p><\/div>\n\t\t\t<div class=\"wp-block-group aa-next-card is-layout-flow wp-block-group-is-layout-flow\"><h3 class=\"wp-block-heading\"><a href=\"https:\/\/www.amyloidosisalliance.org\/nl\/soorten-amyloidose\/attr-amyloidose\/\">ATTR-amylo\u00efdose<\/a><\/h3><p class=\"wp-block-paragraph\">Veroorzaakt door transthyretine: erfelijk bij ATTRv, leeftijdsgebonden bij ATTRwt.<\/p><\/div>\n\t\t<\/div>\n\t\t\n\t<\/div>\n\t\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Home\u203aAmylo\u00efdose\u203aSoorten amylo\u00efdose\u203aAndere soorten Soorten amylo\u00efdose Andere soorten AL-, AA- en ATTR-amylo\u00efdose zijn de meest erkende systemische vormen van amylo\u00efdose. Andere vormen zijn onder meer zeldzame erfelijke amylo\u00efdosen en gelokaliseerde amylo\u00efdose. Twee situaties vallen buiten die beschrijving: erfelijke eiwitten anders dan transthyretine, en afzettingen die het orgaan waarin ze zijn ontstaan nooit verlaten. Ze hebben weinig [&hellip;]<\/p>\n","protected":false},"author":0,"featured_media":0,"parent":3695,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-3665","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.6 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Andere soorten amylo\u00efdose, naast AL, AA en ATTR<\/title>\n<meta name=\"description\" content=\"AL-, AA- en ATTR-amylo\u00efdose zijn de bekendste systemische vormen. 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